Paeds Cases · cardiology
Counsel a young woman with a Fontan circulation on contraception, pregnancy, and staying in care — OSCE
OSCE communication and shared-planning station: a 19-year-old woman with a Fontan circulation returns after a gap in care and asks about contraception and a future pregnancy. The candidate must re-engage her without judgement, advise on safe contraception, counsel realistically on pregnancy risk using the modified WHO classification, address endocarditis prophylaxis, and secure lifelong ACHD follow-up.
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Target exams
Candidate brief (5 minutes to read)
You are the registrar in the adult congenital heart disease clinic. A 19-year-old woman with a single ventricle palliated to a Fontan circulation has returned after a two-year gap in care. She has a new partner, wants advice about contraception, and says she might want children one day. She feels reasonably well but is breathless on stairs. In eight minutes, re-engage her in care without judgement, advise on safe contraception, counsel realistically about a future pregnancy, address endocarditis prophylaxis, and agree a lifelong follow-up plan. [1] [4]
Marking criteria
Communication and relationship (6 marks)
- Re-engages her warmly and without blame for the gap in care; explores why she disengaged and what would help her stay in care. [4]
- Explores her own priorities — the relationship, contraception, and her wish for children — before delivering information, and checks understanding throughout. [1]
- Delivers realistic, potentially unwelcome pregnancy information honestly while holding her hopes and distress; avoids both false reassurance and blunt prohibition. [8]
Content — contraception and pregnancy (8 marks)
- Advises avoiding combined oestrogen-containing contraception because the Fontan circulation carries a high thrombotic risk. [7]
- Recommends progestogen-only methods or long-acting reversible contraception (implant or intrauterine device) as safe and effective, and explains why an effective method matters most in a high-risk lesion. [7]
- Explains that a Fontan circulation is modified WHO class III (high risk) for pregnancy, needing expert shared maternal-cardiac care, and names the real risks of arrhythmia, heart failure, thromboembolism, and adverse fetal outcomes. [8]
- Uses registry-based risk data (for example ROPAC and the CARPREG II score) to give individualised figures rather than vague reassurance, and counsels before conception. [9]
Endocarditis prophylaxis and follow-up (4 marks)
- States that with no prosthetic material or prior endocarditis she does not routinely need antibiotic prophylaxis, and gives the current high-risk indications; emphasises oral hygiene. [11]
- Agrees a lifelong follow-up plan: re-stage the lesion, resume six-to-twelve-monthly ACHD centre review, give a portable summary, and arrange active recall so she is not lost again. [1]
Shared decision and closure (2 marks)
- Summarises the plan, confirms understanding, agrees a contraception choice and a follow-up appointment, and offers a named contact and psychosocial support. [4]
Examiner notes
The discriminating candidate re-engages the patient without a hint of blame, recognising that loss to follow-up is a system failure as much as a patient one, and that this returning patient is a success to protect. On content, the candidate must separate contraception (safe, effective, avoid oestrogen) from pregnancy (high risk, class III, counsel before conception) and must resist two failure modes: falsely reassuring her that pregnancy is fine, or bluntly forbidding it without exploring her values and the shared-care options. Raising endocarditis prophylaxis correctly — that she does not need it — and securing active recall so she is not lost a third time demonstrate the systems thinking the station tests. [8] [4]
References
- [1]Stout KK, Daniels CJ, Aboulhosn JA, Bozkurt B, Broberg CS, et al. 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease J Am Coll Cardiol, 2019.PMID 30121239
- [4]Mackie AS, Ionescu-Ittu R, Therrien J, Pilote L, Abrahamowicz M, Marelli AJ Children and adults with congenital heart disease lost to follow-up: who and when? Circulation, 2009.PMID 19597053
- [7]Regitz-Zagrosek V, Roos-Hesselink JW, Bauersachs J, Blomström-Lundqvist C, Cífková R, et al. 2018 ESC Guidelines for the management of cardiovascular diseases during pregnancy. Eur Heart J, 2018.PMID 30165544
- [8]Canobbio MM, Warnes CA, Aboulhosn J, Connolly HM, Khanna A, et al. Management of Pregnancy in Patients With Complex Congenital Heart Disease: A Scientific Statement for Healthcare Professionals From the American Heart Association. Circulation, 2017.PMID 28082385
- [9]Silversides CK, Grewal J, Mason J, Sermer M, Kiess M, et al. Pregnancy Outcomes in Women With Heart Disease: The CARPREG II Study. J Am Coll Cardiol, 2018.PMID 29793631
- [11]Wilson W, Taubert KA, Gewitz M, Lockhart PB, Baddour LM, et al. Prevention of infective endocarditis: guidelines from the American Heart Association Circulation, 2007.PMID 17446442