Paeds Cases · ent-hearing-and-oral-health
Counsel a family on a small, malformed ear and the hearing pathway — OSCE
OSCE communication and shared decision-making station: explaining the diagnosis of grade III microtia with aural atresia in a newborn with a normal contralateral ear, the meaning of the conductive hearing loss and why the inner ear is spared, the reassuring outlook for speech and language through the good ear, the staged reconstructive pathway across childhood, the role of the Jahrsdoerfer CT score in deciding between atresiaplasty and a bone-conduction device, and the safety-net and multidisciplinary follow-up, in plain language that builds confidence.
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Target exams
Communication tasks
Open by acknowledging the parents' worry and confirming what they have noticed, then explain the diagnosis in plain language: the outer part of the ear did not finish forming on the right while the baby was developing, and the ear canal that should carry sound inward is also closed over — together these are called microtia with aural atresia. Reassure them that the inner ear, the part that actually hears, is almost always formed normally in this condition, so the problem is one of conducting sound inward, not of the hearing nerve itself. [1]
Address the fear of deafness directly. Because the left ear hears normally, their daughter will develop spoken language on time; she will need audiology to confirm this, and she may find it a little harder to locate sound or to hear in noisy classrooms, but she is not deaf. Explain the newborn hearing screen result as the expected consequence of the closed canal, not as a separate hearing-nerve problem. [11]
Outline the pathway honestly. The ear can be rebuilt, and there are options — rebuilding it from her own rib cartilage, or using a synthetic framework — but this is planned for around six to ten years of age, when she is big enough and the other ear is near its adult size, so there is no rush now. For the hearing on the right side, when she is older the team will do a scan that scores the anatomy out of ten; a good score means an operation to open a canal may be possible, and a lower score means a small bone-conduction hearing device is the safer and equally effective choice. All of this is decided with the family over years, not weeks. [8] [3]
Close with a clear plan and safety-net. Arrange a formal hearing test (ABR) to confirm the good left ear, and refer the family to the multidisciplinary craniofacial team who will coordinate audiology, the ear and plastic surgeons, genetics, speech and psychology across her childhood. Bring her back sooner if there is any concern about the good ear or her hearing or speech. Invite questions, confirm understanding, and set the first follow-up. [1]
References
- [1]Camison L; Lisk RC; Soldanska M Microtia: A Review. Clin Plast Surg, 2025.PMID 39986885
- [3]Jahrsdoerfer RA; Yeakley JW; Aguilar EA; Cole RR; Gray LC Grading system for the selection of patients with congenital aural atresia. Am J Otol, 1992.PMID 1598988
- [11]Cywka KB; Krol B; Skarzynski PH Effectiveness of Bone Conduction Hearing Aids in Young Children with Congenital Aural Atresia and Microtia. Med Sci Monit, 2021.PMID 34561413
- [8]Kim HAJ; Namavarian A; Khan U; Levy BB; Ziai H; et al Reconstructive Techniques in Pediatric Congenital Microtia: A Systematic Review and Meta-analysis. Facial Plast Surg, 2025.PMID 38232751