Psych Vivas · Consultation-liaison psychiatry
Huntington disease psychiatry — structured clinical viva
Fellowship viva on HD neuropsychiatry, suicide, irritability algorithms, and VMAT2–mood interface.
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Target exams
Interpretation
Reveal interpretation
Leading diagnoses: HD-related major depression with passive SI plus irritability/aggression, possible apathy overlap, on background of manifest HD; consider tetrabenazine-related dysphoria after recent titration.[1][2][5]
Differentials to voice: delirium/infection; pure apathy; primary mood disorder coincidental; substance use; emerging psychosis.[3][7]
Acute plan: structured suicide assessment and safety planning; collateral for aggression; joint neurology review of VMAT2 dose; start SSRI for depression/irritability if indicated (e.g. sertraline low start); escalate to low-dose SGA if severe aggression/psychosis; non-drug structure and carer support.[2][3][4]
Chorea drugs: TETRA-HD/FIRST-HD literacy — benefit for chorea, monitor depression/parkinsonism.[5][6]
Ethics: do not casually predictively test asymptomatic minors for adult-onset HD; support adult relatives through counselling pathways.[7]
Close: multidisciplinary HD clinic, advance care planning while capacity intact, ongoing suicide surveillance.[3][7]
Key points
References
- [1]van Duijn E, Craufurd D, Hubers AA, et al. Neuropsychiatric symptoms in a European Huntington's disease cohort (REGISTRY) J Neurol Neurosurg Psychiatry, 2014.PMID 24828898
- [2]Hubers AA, van Duijn E, Roos RA, et al. Suicidal ideation in a European Huntington's disease population J Affect Disord, 2013.PMID 23876196
- [3]Anderson KE, van Duijn E, Craufurd D, et al. Clinical Management of Neuropsychiatric Symptoms of Huntington Disease: Expert-Based Consensus Guidelines on Agitation, Anxiety, Apathy, Psychosis and Sleep Disorders J Huntingtons Dis, 2018.PMID 30040737
- [4]Groves M, van Duijn E, Anderson K, et al. An International Survey-based Algorithm for the Pharmacologic Treatment of Irritability in Huntington's Disease PLoS Curr, 2011.PMID 21975525
- [5]Huntington Study Group Tetrabenazine as antichorea therapy in Huntington disease: a randomized controlled trial Neurology, 2006.PMID 16476934
- [6]Huntington Study Group, Frank S, Testa CM, et al. Effect of Deutetrabenazine on Chorea Among Patients With Huntington Disease: A Randomized Clinical Trial JAMA, 2016.PMID 27380342
- [7]Walker FO Huntington's disease Lancet, 2007.PMID 17240289